Anesthetic Management of a Patient with Pompe Disease: Our Experiment
Abstract
Pompe disease is a fatal autosomal recessive glicogen storage disease presenting with hypertrophic cardiomyopathy, widespread myopathy and hypotonia. In this presentation, we aimed to present our anesthetic approach to 12 teeth extraction planned non-cooperative, 34-month-old patient who were being followed-up in an external center with Infantile Pompe Disease.
References
-Kishnani P, Howell RR. Pompe disease in infants and children. J Pediatrics 2004;144:35-43.
-Raben N, Plotz P, Byrne BJ. Acid alpha-glucosidase deficiency (glycogenosis type II, Pompe disease). Curr Mol Med 2002;2:145-66. 3.
-Tan D, Xu J, Yang Y, Gu M, Yu X. Postoperative acute respiratory failure caused by adultonset pompe disease. Clin Respir J. 2016 Jun 20. doi: 10.1111/crj.12514.
-Al Atassi A, Al Zughaibi N, Naeim A, Al Basha A, Dimitriou V. Anesthesia Management In An Infant With Glycogen Storage Disease Type II (Pompe Disease). Middle East J Anaesthesiol. 2015;23:343-6.
-Doğan O, Unver S, Tunçel YI, Keleş S, Süner ZC. Monitörize Anestezi Bakımında Deksmedetomidin ile Midazolam/Remifentanil KombinasyonununKarşılaştırılması. Türk Anest Rean Der Dergisi 2011; 39:292-301.
- Arpaci AH, Isik B. Pediatric tooth extractions under sedoanalgesia. Pak J Med Sci. 2016;32:1291-5.
