Anesthetic Management of a Patient with Pompe Disease: Our Experiment

  • Ayşe Hande Arpacı
  • Ozan Kaan Venedik resident
Keywords: Pompe disease, sedoanalgesia, monitorized anesthesia care


Pompe disease is a fatal autosomal recessive glicogen storage disease presenting with hypertrophic cardiomyopathy, widespread myopathy and hypotonia. In this presentation, we aimed to present our anesthetic approach to 12 teeth extraction planned non-cooperative, 34-month-old patient who were being followed-up in an external center with Infantile Pompe Disease. 


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