Hirschsprung’s Disease Masquerading as Obstructing Congenital Band in a Premature Neonate: A Double Pathology
Abstract
Chronic Feeding intolerance in preterm infants is often associated with necrotizing enterocolitis rather than Hirschsprung’s disease (HD) or intestinal obstruction due to congenital band. We report a case of a 26-day-old male born premature at 30 weeks of gestation presenting with recurrent episodes of desaturation and feeding intolerance which were initially thought to be due to NEC. However, the pathology was found to be a congenital band that caused partial intestinal obstruction and suction rectal biopsy subsequently showed it had characteristic features of HD. This dual pathology is a rare condition that required a high index of suspicion to be able to get a correct diagnosis especially in a premature baby with non-resolving chronic feeding intolerance or chronic partial obstruction.References
Sharp NE, Pettiford-Cunningham J, Shah SR, Thomas P, Juang D, Peter SDS, et al. The Prevalence of Hirschsprung Disease In Premature Infants After Suction Rectal Biopsy. Journal of Surgical Research. 2013; 184: 374-7
Lewis NA, Levitt MA, Zallen GS, Zafar MS, Iacono KL, Rossman JE, et al. Diagnosing Hirschsprung's Disease: Increasing The Odds Of A Positive Rectal Biopsy Result. Journal of Pediatric Surgery. 2003; 38: 412-6
Haricharan RN, Georgeson KE, editors. Hirschsprung disease. Seminars in Pediatric Surgery; 2008: Elsevier
Liu C, Wu T-C, Tsai H-L, Chin T, Wei C. Obstruction Of The Proximal Jejunum By An Anomalous Congenital Band—A Case Report. Journal of Pediatric Surgery. 2005; 40: E27-E9.
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Published
20.12.2018
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Case Report