Cystic Lymphangioma: A Rare Disease of the Adrenal Gland

  • Nor Faezan Abdul Rashid Universiti Technology MARA, UiTM
  • Rohaizak Muhammad
  • Suraya Othman
  • Shahrun Niza Abdullah Suhaimi
  • Norasyikin A Wahab
Keywords: Cystic adrenal lymphangioma, adrenalectomy, adrenal, cyst, lymphangioma

Abstract

Cystic adrenal neoplasms are uncommon and may be discovered incidentally or may be symptomatic but cystic lymphangioma is a rare benign tumour. The tumour usually occurs in the neck or axilla and rarely involves the adrenal gland. Here we report a case of a 42-year-old lady presented with symptoms of anorexia, vomiting and lethargy for 3 weeks. Apart from evidence of mild dehydration, there was no positive physical examination. Upon admission, her blood urea and creatinine was high and she was diagnosed with end stage renal disease secondary to chronic glomerulonephritis. Ultrasound of the abdomen revealed an incidental right adrenal mass and computed tomography (CT) scan showed a lesion with Hounsfield unit (HU) of 13, 20 and 21 on plain, venous and delayed phase, giving an absolute wash out of 12.5%. Biochemical tests were consistent with a non-functioning adrenal incidentaloma. Hence she was subjected for right retroperitoneoscopic adrenalectomy in view of suspicious of adrenal malignancy. However, histopathology reported as a rare adrenal cystic lymphangioma.

Author Biography

Nor Faezan Abdul Rashid, Universiti Technology MARA, UiTM
Department of SurgeryLecturer

References

Erickson LA, Lloyd RV, Hartman R, Thompson G. Cystic adrenal neoplasms. Cancer. 2004;101(7):1537-44.

Joliat GR, Melloul E, Djafarrian R, Schmidt S, Fontanella S, Yan P, Demartines N, Halkic N. Cystic lymphangioma of the adrenal gland: report of a case and review of the literature. World journal of surgical oncology. 2015;13:58.

Van Oudheusden TR, Nienhuijs SW, Demeyere TB, Luyer MD, de Hingh IH. Giant cystic lymphangioma originating from the lesser curvature of the stomach. World journal of gastrointestinal surgery. 2013;5:264.

Ellis CL, Banerjee P, Carney E et al. Adrenal lymphangioma: clinicopathologic and immunohistochemical characteristics of a rare lesion. Hum Pathol. 2011; 42: 1013-8

Ates LE, Kapran Y, Erbil Y et al. Cystic lymphangioma of the right adrenal gland. Pathol Oncol Res. 2005; 11: 242-4

Zhao M, Gu Q, Li C, Yu J, Qi H. Cystic lymphangioma of adrenal gland: a clinicopathological study of 3 cases and review of literature. International journal of clinical and experimental pathology. 2014;7:5051.

Faten Hadjkacem, Mouna Ammar, Ayman Maalej et al. Cystic lymphangioma of the adrenal gland: A case report and a review of the literature. American Journal of Medicine Studies. 2015; 3: 1-3

Poncelet V. Retroperitoneal cystic lymphangioma. Journal Belge Radiol. 1998. 81:245

Geramizadeh B, Yazdanpanah S, Salahi H, Marzban M. Adrenal Cystic Lymphangioma Presented With Hypertension: A Case Report. Nephro-urology monthly. 2015;7: :e27049.

Liu B, Li Y, Wang S. Adrenal lymphangioma removed by a retroperitoneoscopic procedure. Oncol Lett. 2013;5:539–40

Published
2017-12-22