Cystic Lymphangioma: A Rare Disease of the Adrenal Gland

  • Nor Faezan Abdul Rashid Universiti Technology MARA, UiTM
  • Rohaizak Muhammad
  • Suraya Othman
  • Shahrun Niza Abdullah Suhaimi
  • Norasyikin A Wahab
Keywords: Cystic adrenal lymphangioma, adrenalectomy, adrenal, cyst, lymphangioma


Cystic adrenal neoplasms are uncommon and may be discovered incidentally or may be symptomatic but cystic lymphangioma is a rare benign tumour. The tumour usually occurs in the neck or axilla and rarely involves the adrenal gland. Here we report a case of a 42-year-old lady presented with symptoms of anorexia, vomiting and lethargy for 3 weeks. Apart from evidence of mild dehydration, there was no positive physical examination. Upon admission, her blood urea and creatinine was high and she was diagnosed with end stage renal disease secondary to chronic glomerulonephritis. Ultrasound of the abdomen revealed an incidental right adrenal mass and computed tomography (CT) scan showed a lesion with Hounsfield unit (HU) of 13, 20 and 21 on plain, venous and delayed phase, giving an absolute wash out of 12.5%. Biochemical tests were consistent with a non-functioning adrenal incidentaloma. Hence she was subjected for right retroperitoneoscopic adrenalectomy in view of suspicious of adrenal malignancy. However, histopathology reported as a rare adrenal cystic lymphangioma.

Author Biography

Nor Faezan Abdul Rashid, Universiti Technology MARA, UiTM
Department of SurgeryLecturer


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