Undifferentiated Embryonal Sarcoma of the Liver: An Enigma of Diagnosis

  • Affirul Chairil Ariffin Department of Surgery, Universiti Sains Islam Malaysia, Kuala Lumpur, Malaysia
  • Firdaus Hayati Department of Surgery, Faculty of Medicine and Health Sciences, Universiti Malaysia Sabah, Kota Kinabalu, Sabah
  • Nornazirah Azizan Department of Pathobiology and Medical Diagnostic, Faculty of Medicine and Health Sciences, Universiti Malaysia Sabah, Kota Kinabalu, Sabah
  • Zamri Zuhdi Department of Surgery, Universiti Kebangsaan Malaysia, Kuala Lumpur, Malaysia
  • Azlanuddin Azman Department of Surgery, Universiti Kebangsaan Malaysia, Kuala Lumpur, Malaysia
  • Hairol Azrin Othman Department of Surgery, Universiti Kebangsaan Malaysia, Kuala Lumpur, Malaysia
  • Razman Jarmin Department of Surgery, Universiti Kebangsaan Malaysia, Kuala Lumpur, Malaysia
Keywords: Abscess, liver, embryonal, sarcoma

Abstract

A 20-year-old man presented with peritonitis requiring emergency laparotomy. He was found to have a huge liver abscess on the right lobe. Open drainage was performed but the abscess was persistently unresolved upon follow up. Computed tomography (CT) revealed a solid liver lesion with raised Ca 19-9. Right hepatectomy was subjected and histology was consistent with a rare and aggressive case of embryonal sarcoma of the liver. Despite oncologic resection, he developed local recurrence and succumbed to death in 6 month postoperatively. We describe a unique aetiology of liver abscess with literature reviews of undifferentiated embryonal sarcoma of the liver.

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Published
2018-09-22